Skip to main content

Table 2 European League Against Rheumatism (EULAR)-Definitions of AAV-Phenotypes (localized, early-systemic, generalized) and disease courses (serious, refractory) [42, 43]

From: Cerebral involvement in systemic vasculitides

Localized upper and/or lower respiratory tract +/−
Early systemic without impaired organ function or life-threatening disease +
Generalized disease with impairment of renal or other organ function, Creatinine < 500 μmol/l +
Serious renal or vital organ failure, Creatinine ≥500 μmol/l +
Refractory progressive disease which does not respond to standard therapy +
  1. Abbreviations: + ANCA-positive,  ANCA-negative