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Table 1 Classification of Systemic Vasculitides according to Vessel size [27]

From: Cerebral involvement in systemic vasculitides

Large

 – Giant cell arteriitis (GCA)

 – Takayasu-Arteriitis (TA)

Medium

 – Polyarteriitis nodosa (PAN)

 – Kawasaki-Disease (KD)

Small (with ANCA)

 – Granulomatous with polyangiitis (GPA)

 – Microscopic polyangiitis (MPA)

 – Eosinophilic granuomatous with polyangiitis (EGPA)

Small (with immunocomplexes)

 – Cryoglobulinemic vasculitis (CV)

 – Behçet-Syndrome (BD)

 – Collagene vascular disease (SLE, MCTD, SS)